Association of a Cor Triatriatum Sinister and a right partial anomalous pulmonary venous return. A case report.
نویسندگان
چکیده
A 56-day old baby girl referred for recurrent respiratory tract infections and stridor, showed a rare association of a Cor Triatriatum Sinister (CTS) and a right Partial Anomalous Pulmonary Venous Return (PAPVR), in the form of a stenosed Scimitar vein, draining the right pulmonary veins to the subdiaphragmatic inferior vena cava (IVC), on echography and angiography. The baby underwent successful surgical repair of the CTS, by resection of the obstructive false membrane and reconnection of the Scimitar vein to the left atrium. At the age of 5 years, the child is doing well without any evidence of obstruction on the right or the left pulmonary venous drainage.
منابع مشابه
Cor Triatriatum Sinistrum Presenting as Cyanotic Congenital Heart Disease A Rare Case Report
Cor triatriatum is an acyanotic congenital heart disease. We present a rare case of cor triatriatum sinistrum in a 6-month-old female infant who was presented with cyanosis and failure to thrive. The 2D transthoracic echocardiography and the Doppler color flow imaging showed a proximal venous chamber communicating to the distal left atrium through restrictive opening to the low-pressure, dis...
متن کاملIMAGES in PAEDIATRIC CARDIOLOGY
Cor triatriatum sinister is a rare congenital cardiac malformation characterized by a membrane in the left atrium which separates the left atrium into the proximal and distal chambers.Association of cor triatriatum is extremely rare with situs inversus totalis. Here we report a rare case of cor triatriatum sinister with situs inversus totalis in a 5 month old female infant. MeSH: Cor triatriatu...
متن کاملPulmonary-Esophageal Variceal Bleeding: A Unique Presentation of Partial Cor Triatriatum Sinistrum
Cor triatriatum sinistrum is a rare congenital disorder defined as a division of the left atrium by a diaphragmatic membrane resulting in two left atrial chambers. The membranous division of the atrium can be partial or complete and can affect either atrium, with involvement of the right atrium referred to as cor triatriatum dexter. The presence of fenestrations within the membrane allows for c...
متن کاملCor triatriatum sinister, not mitral stenosis, in an adult with previous Sydenham's chorea: diagnosis and preoperative assessment by cross sectional echocardiography.
In cor triatriatum sinister, one of the rarest congenital cardiac anomalies, a membrane divides the left atrium into a pulmonary venous component above and the vestibule below. The importance of the anomaly lies in the effects of the resultant pulmonary venous obstruction that usually present in the first year of life and can mimic obstructed total anomalous venous drainage or congenital mitral...
متن کاملSuccessful Multi-chamber Catheter Ablation of Persistent Atrial Fibrillation in Cor Triatriatum Sinister
Cor triatriatum sinister is a rare congenital cardiac anomaly with an incidence of between 0.1 and 0.4% [1,2] whereby the left atrium is functionally and anatomically divided into two separate chambers by a thin membrane. Although there are a limited number of reports of successful ablation of left atrial focal tachycardia and simple pulmonary vein isolation in individuals with cor triatriatum ...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- Acta chirurgica Belgica
دوره 105 2 شماره
صفحات -
تاریخ انتشار 2005